๐Ÿซ Chapter 434 ยท Congenital Anomalies of the Larynx, Trachea, and Bronchi

Nelson Textbook of Pediatrics 22nd Edition | Laryngomalacia (most common, 45-75%), subglottic stenosis, vocal cord paralysis, laryngeal webs/atresia, subglottic hemangioma, saccular cysts, laryngeal cleft, tracheomalacia, vascular rings (double aortic arch, pulmonary artery sling), tracheal stenosis, foregut cysts. Diagnosis: flexible laryngoscopy, bronchoscopy, CT/MRI/angiography. Management: observation (most laryngomalacia), supraglottoplasty, propranolol for hemangioma, surgical repair of stenoses/vascular rings.

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๐Ÿ“‹ 30 Clinical Scenarios โ€” Congenital Airway Anomalies

๐Ÿ“‡ Highโ€‘Yield Cards: Congenital Larynx/Trachea/Bronchi (Chap 434)

๐Ÿฉบ Interactive Clinical Approach: Stridor & Congenital Airway Lesions

Select a presentation for diagnostic approach and management.

๐Ÿ“‹ Stepwise Management of Congenital Airway Anomalies

    AnomalyDiagnosisTreatment
    LaryngomalaciaAwake flexible laryngoscopy (omega epiglottis, short aryepiglottic folds)Observation (90%), supraglottoplasty if severe
    Subglottic stenosisBronchoscopy (Myer-Cotton grading)Mild: observe; severe: laryngotracheal reconstruction, cricotracheal resection
    Vocal cord paralysisAwake flexible laryngoscopy (immobile cord)Unilateral: often resolves; bilateral: tracheostomy, later glottic widening
    Subglottic hemangiomaBronchoscopy, MRIPropranolol (first-line), steroids, laser, tracheostomy
    TracheomalaciaFlexible bronchoscopy (dynamic collapse)Observation, CPAP, aortopexy if severe
    Vascular ringBarium swallow, CT angiography, MRISurgical division of ring

    โšก Reflex Prompts โ€” Congenital Airway Obstruction

    ๐Ÿ“– Summary: Congenital Airway Anomalies โ€” Nelson 22nd Ed